Thelansis

  Clear cell sarcoma (CCS) is a rare type comprising approximately 1% of all soft tissue sarcomas. Clear cell sarcoma is localized mainly in the lower limbs, with the majority of cases localized in the area of the foot and ankle, where up to 40% of tumors are located. The upper limb is affected in 25% of cases. Primary CCS tumors usually develop deeply in soft tissues, adjacent to tendons, fasciae, or dissections. CCS can develop at any age, however, a number of cases of CCS have been diagnosed over the age of 40 years. Despite slow growth and latent progression, CCS is characterized by high aggressiveness — in about 30% of patients, lymph nodes or distant metastases are present at the time of diagnosis. Unlike most sarcomas that metastasize via the circulatory system approximately 50% of patients with CCS present with metastases in the lymph nodes. The vast majority of categories of sarcomas had an incidence case ranges between 1 to 5 cases per 1,000,000. The most common were le...